Cochleovestibular Syndrome as an Atypical Manifestation of Neuro-Behçet’s Disease

Behcet’s disease (BD) is a chronic multisystem disorder that can affect the skin, mucous membrane, and central nervous system. It can be characterized by symptoms such as cognitive impairments, psychiatric symptoms, and focal neurologic deficits, we present the case of a 56 years old neuro-BD with a 16 years history of cephalea, diplopia, generalized tonicoclonic comital seizures and amnesia stabilized on azathioprine 6 months later he developed a brutal deafness associated with tinnitus of the left ear and a spontaneous vertigo. This case report points out to the diagnostic and therapeutic challenges of BD especially when unusual symptoms are the prominent manifestations of the disease. It also discusses the different therapeutic options for patients with BD and cochleovestibular symptoms.