ATYPICAL PAEDIATRIC EXTRA VENTRICULAR NEUROCYTOMA– A RARE CASE REPORT

Central neurocytoma (CN) and extra ventricular neurocytoma (EVN) are rare intracranial tumors. Central neurocytomas are well-differentiated, intraventricular lesions mainly seen in adults. Similar tumors may develop in the brain parenchyma or spinal cord referred to as extra ventricular neurocytomas. Here we are reporting a case of 10-year-old boy with intracranial mass lesion for which left parieto-occipital craniotomy was done with histopathology showing atypical extra ventricular neurocytoma, recurred after for which gross total excision was done and histopathology report confirmed neurocytoma recurrence. Postoperative MRI showed residual disease and treated with radiation therapy 50 Gray in 28 fractions using IMRT technique. Post radiation MRI showed no residual disease and was kept under follow up.