Morphea: insights into a rare skin condition

KeypointsWhat is known -Morphea is a rare connective tissue disease, characterized by skin inflammation and fibrosis.-Genetic predisposition, immune dysregulation, and environmental factors are recognized triggers.-Treatment can be challenging, especially in moderate to severe cases requiring systemic therapy.What is added -Morphea can present with characteristic painful lesions in pediatric patients.-A multidisciplinary approach, involving dermatology, is essential for accurate diagnosis and management.-Although diagnosis is clinical, skin biopsies are useful for confirming the diagnosis, especially in complex cases.

Authors

Publication Details

Journal
Portuguese Journal of Pediatrics
Published
2025-05-27
DOI
https://doi.org/10.24875/pjp.24000078
Primary Topic
Systemic Sclerosis and Related Diseases
Type
article
Field-Weighted Citation Impact
0.00
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article

Morphea: insights into a rare skin condition

Sara Fonseca, Catarina Macedo Francisco, Joana Frade, Isabel Correia
Portuguese Journal of Pediatrics
Systemic Sclerosis and Related Diseases
article

Morphea: insights into a rare skin condition

Sara Fonseca, Catarina Macedo Francisco, Joana Frade, Isabel Correia
article en

Abstract

KeypointsWhat is known -Morphea is a rare connective tissue disease, characterized by skin inflammation and fibrosis.-Genetic predisposition, immune dysregulation, and environmental factors are recognized triggers.-Treatment can be challenging, especially in moderate to severe cases requiring systemic therapy.What is added -Morphea can present with characteristic painful lesions in pediatric patients.-A multidisciplinary approach, involving dermatology, is essential for accurate diagnosis and management.-Although diagnosis is clinical, skin biopsies are useful for confirming the diagnosis, especially in complex cases.

Portuguese Journal of Pediatrics
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Openalex Percentile: Top 83%
Systemic Sclerosis and Related Diseases
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