Morphea: insights into a rare skin condition
KeypointsWhat is known -Morphea is a rare connective tissue disease, characterized by skin inflammation and fibrosis.-Genetic predisposition, immune dysregulation, and environmental factors are recognized triggers.-Treatment can be challenging, especially in moderate to severe cases requiring systemic therapy.What is added -Morphea can present with characteristic painful lesions in pediatric patients.-A multidisciplinary approach, involving dermatology, is essential for accurate diagnosis and management.-Although diagnosis is clinical, skin biopsies are useful for confirming the diagnosis, especially in complex cases.
Authors
- Sara Fonseca (ORCID: https://orcid.org/0000-0002-8270-767X)
- Catarina Macedo Francisco (ORCID: https://orcid.org/0000-0002-4540-9307)
- Joana Frade (ORCID: https://orcid.org/0000-0002-5471-7889)
- Isabel Correia (ORCID: https://orcid.org/0000-0002-0809-3040)
Publication Details
- Journal
- Portuguese Journal of Pediatrics
- Published
- 2025-05-27
- DOI
- https://doi.org/10.24875/pjp.24000078
- Primary Topic
- Systemic Sclerosis and Related Diseases
- Type
- article
- Field-Weighted Citation Impact
- 0.00