Reduced pulmonary arterial compliance predicts poor short-term outcome in children with pulmonary arterial hypertension independent of pulmonary vascular resistance
The relationship between PACi and PVRi is not constant. PACi is associated with disease severity and predicts short term outcome in children with IPAH/HPAH independent of PVRi and mPAP. Therefore, PACi is of additional prognostic value to PVRi, especially for short term prediction.
Authors
- Johannes M. Douwes (ORCID: https://orcid.org/0000-0003-3146-5831)
- Rolf M.F. Berger (ORCID: https://orcid.org/0000-0002-4385-5784)
- Meindina G. Haarman (ORCID: https://orcid.org/0000-0002-1223-6067)
- Mark‐Jan Ploegstra (ORCID: https://orcid.org/0000-0002-3017-746X)
- Marcus T.R. Roofthooft
- Eva Gouwy
Institutions
- University Medical Center Groningen (NL)
- University of Groningen (NL)
Publication Details
- Journal
- Frontiers in Cardiovascular Medicine
- Published
- 2025-05-22
- DOI
- https://doi.org/10.3389/fcvm.2025.1526435
- Citations
- 1
- Primary Topic
- Pulmonary Hypertension Research and Treatments
- Type
- article
- Field-Weighted Citation Impact
- 1.52