Data‐Driven Clustering Approach to Identify Different Phenotypes of Primary Central Nervous System Vasculitis
This unsupervised analysis of a large PCNSV cohort identified two different clinical and radiological phenotypes with different diagnostic work-ups, which confirms the relevance of distinguishing PCNSV phenotypes according to the sizes of affected vessels.
Authors
- Anaïs R. Briant (ORCID: https://orcid.org/0009-0005-2361-1490)
- Hubert de Boysson (ORCID: https://orcid.org/0000-0001-9083-8365)
- Nelly Dequatre (ORCID: https://orcid.org/0000-0003-2153-1436)
- Sophie Godard
- Achille Aouba (ORCID: https://orcid.org/0000-0003-1726-3811)
- Emmanuel Touzé (ORCID: https://orcid.org/0000-0002-7254-2162)
- Laurent Derex (ORCID: https://orcid.org/0000-0002-0909-8900)
- T. Papo (ORCID: https://orcid.org/0000-0002-7481-5099)
- Adil Maarouf (ORCID: https://orcid.org/0000-0002-6755-496X)
- Olivier Detante (ORCID: https://orcid.org/0000-0001-8761-3288)
- Jean‐Jacques Parienti (ORCID: https://orcid.org/0000-0002-4774-5590)
- Jean Capron (ORCID: https://orcid.org/0000-0003-1788-8897)
- Nicolas Lambert (ORCID: https://orcid.org/0000-0002-6660-0100)
- Cédric Gollion (ORCID: https://orcid.org/0000-0001-6098-2569)
- Christian Denier (ORCID: https://orcid.org/0000-0002-2087-5563)
- B. Guillon (ORCID: https://orcid.org/0000-0002-7539-7263)
- Alexis Régent (ORCID: https://orcid.org/0000-0002-8136-2454)
- Sylvain Lanthier (ORCID: https://orcid.org/0000-0001-9762-5514)
- Sonia Alamowitch (ORCID: https://orcid.org/0000-0002-0074-3520)
- Lisa Humbertjean
- Stéphane Vannier (ORCID: https://orcid.org/0000-0002-4344-9102)
- Barbara Casolla (ORCID: https://orcid.org/0000-0003-4199-995X)
- Grégoire Boulouis (ORCID: https://orcid.org/0000-0001-8422-9205)
- Alexandre Yves Poppe (ORCID: https://orcid.org/0000-0002-1419-2635)
- Caroline Arquizan (ORCID: https://orcid.org/0000-0001-7347-1039)
- Philippe Kerschen
- Igor Sibon (ORCID: https://orcid.org/0000-0002-1171-4215)
- Mathieu Zuber (ORCID: https://orcid.org/0000-0002-4049-2746)
- Laurent Kremer (ORCID: https://orcid.org/0000-0002-7246-2533)
- Amina Sellimi (ORCID: https://orcid.org/0000-0002-8338-3814)
- Ahmad Nehme (ORCID: https://orcid.org/0000-0002-7700-6799)
- David Weisenburger‐Lile
- Benjamin Terrier (ORCID: https://orcid.org/0000-0001-6612-7336)
- Christian Pagnoux
- Clothilde Isabel
- Antoine Néel (ORCID: https://orcid.org/0000-0002-7707-5794)
Institutions
- Mount Sinai Hospital (CA)
- Inserm (FR)
- Centre Hospitalier de Luxembourg (LU)
- University of Toronto (CA)
- Centre Hospitalier Universitaire de Grenoble (FR)
- Centre Hospitalier Universitaire de Bordeaux (FR)
- Centre Hospitalier Universitaire de Lille (FR)
- Centre Hospitalier Universitaire de Nice (FR)
- Centre Hospitalier Universitaire de Nantes (FR)
- Centre Hospitalier Universitaire de Toulouse (FR)
- Sorbonne Université (FR)
- Hôpital Cochin (FR)
- Centre Hospitalier Universitaire de Montpellier (FR)
- Centre Hospitalier Universitaire de Tours (FR)
- Centre Hospitalier Régional et Universitaire de Nancy (FR)
- Hospices Civils de Lyon (FR)
- Centre Hospitalier Universitaire d'Angers (FR)
- Centre Hospitalier Universitaire de Caen Normandie (FR)
- Pitié-Salpêtrière Hospital (FR)
- Centre Hospitalier Sainte-Anne (FR)
- Centre Hospitalier Universitaire de Liège (BE)
- Hôpital Paris Saint-Joseph (FR)
- Hôpital du Sacré-Cœur de Montréal (CA)
- Centre Hospitalier de l’Université de Montréal (CA)
- Hôpital Bichat-Claude-Bernard (FR)
- Grenoble Institute of Neurosciences (FR)
- Institut du Cerveau (FR)
- Centre Hospitalier Universitaire de Rennes (FR)
- Hôpital Foch (FR)
- Centre hospitalier régional de la Citadelle (BE)
- Hôpital de la Timone (FR)
- Bicêtre Hospital (FR)
- Université Grenoble Alpes (FR)
- Université de Caen Normandie (FR)
Publication Details
- Journal
- European Journal of Neurology
- Published
- 2025-05-01
- DOI
- https://doi.org/10.1111/ene.70174
- Primary Topic
- Vasculitis and related conditions
- Type
- article
- Field-Weighted Citation Impact
- 0.00