Histiocytoid Sweet Syndrome With Paradoxical Neutropenia in a Pediatric Patient

Histiocytoid Sweet syndrome (HSS) is a rare inflammatory skin condition characterized by the infiltration of mononuclear cells in the dermis and leukocytosis with neutrophilia. This uncommon variant of classic Sweet syndrome is rarely reported in the literature, especially in pediatric patients. We present a case of an 8-month-old boy who developed idiopathic HSS along with autoimmune neutropenia. This report adds to the understanding and management of HSS with neutropenia in pediatric patients.