Surgical Management of a Patient With Non-Fallot-Type Absent Pulmonary Valve Syndrome
We describe the presentation and management of an infant with the unique constellation of a massive patent ductus arteriosus, severely insufficient pulmonary valve, hypoplastic tricuspid valve, and a resultant profoundly dilated and hypertrophic right ventricle with intact interventricular septum. Surgery consisted of ductal ligation and division, homograft patch augmentation of the aortic arch, modified Blalock-Taussig-Thomas shunt placement, right ventricle-to-pulmonary artery homograft placement, and atrial septectomy.
Authors
- Matthew L. Stone
- Megan Albertz (ORCID: https://orcid.org/0000-0003-3620-9271)
- Jason J. Breithaupt (ORCID: https://orcid.org/0000-0002-6843-6586)
- Brian Mejak
- Ryan Leahy
- Dale A. Burkett (ORCID: https://orcid.org/0000-0002-2934-315X)
- John S. Kim (ORCID: https://orcid.org/0000-0002-7403-222X)
- Charles D. Fraser (ORCID: https://orcid.org/0000-0003-4761-3296)
Institutions
- Children's Hospital Colorado (US)
- University of Colorado Anschutz Medical Campus (US)
- University of Colorado Denver (US)
Publication Details
- Journal
- World Journal for Pediatric and Congenital Heart Surgery
- Published
- 2025-04-15
- DOI
- https://doi.org/10.1177/21501351251327214
- Primary Topic
- Congenital Heart Disease Studies
- Type
- article
- Field-Weighted Citation Impact
- 0.00