Scimitar Syndrome: A Fortuitous Diagnosis in an Asymptomatic Adult

Scimitar syndrome is a group of cardiopulmonary malformations where the most prominent anomaly is an abnormal venous return affecting mostly the right lung. There are two clinical presentations: infants and adult forms, where the first one is the most severe. The diagnosis is suspected initially by a chest x-ray and confirmed by chest CT-angiography or MR-angiography. Cardiac examinations can help detect associated malformations. The treatment depends on the clinical form and the associated abnormalities, and can range from a simple monitoring to surgical intervention. We report the case of a 45-year-old woman, consulting for an isolated dry cough, whose chest x-ray showed a hypoplastic right lung, with displacement of the heart to the right side, and abnormal retro-cardiac opacity. complementary chest CT-angiography revealed an abnormal dilated vein joining the inferior veina cava as well as other features that allowed us to diagnose the patient with a scimitar syndrome.