Dermatomyositis: A Multifaceted Autoimmune Connective Tissue Disorder: Series of Seven Cases

Dermatomyositis is a rare connective tissue disorder having a wide array of characteristic cutaneous and systemic manifestations. There is an established paraneoplastic association of malignancy with dermatomyositis which is seen in adult patients as compared to juvenile (with an increased risk of malignancy in 15%–30% cases in adult dermatomyositis, without any increased risk of association in juvenile dermatomyositis), which can be seen in our case series. There is also a case linking neurological associations of dermatomyositis to generalized tonic–clonic seizures. We discuss the importance of dermatomyositis, as a potential differential diagnosis among the cases presenting with bulbar symptoms such as dyspnea and dysphagia which can be life-threatening.

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Journal
Clinical Dermatology Review
Published
2025-04-01
DOI
https://doi.org/10.4103/cdr.cdr_108_24
Primary Topic
Inflammatory Myopathies and Dermatomyositis
Type
article
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article

Dermatomyositis: A Multifaceted Autoimmune Connective Tissue Disorder: Series of Seven Cases

Varesh R. Patel, Pooja Agarwal, Kalgi Baxi, Mrunali Anil Joshi et al.
Clinical Dermatology Review
Inflammatory Myopathies and Dermatomyositis
article

Dermatomyositis: A Multifaceted Autoimmune Connective Tissue Disorder: Series of Seven Cases

Varesh R. Patel, Pooja Agarwal, Kalgi Baxi, Mrunali Anil Joshi, Raju G. Chaudhary
article en

Abstract

Dermatomyositis is a rare connective tissue disorder having a wide array of characteristic cutaneous and systemic manifestations. There is an established paraneoplastic association of malignancy with dermatomyositis which is seen in adult patients as compared to juvenile (with an increased risk of malignancy in 15%–30% cases in adult dermatomyositis, without any increased risk of association in juvenile dermatomyositis), which can be seen in our case series. There is also a case linking neurological associations of dermatomyositis to generalized tonic–clonic seizures. We discuss the importance of dermatomyositis, as a potential differential diagnosis among the cases presenting with bulbar symptoms such as dyspnea and dysphagia which can be life-threatening.

Clinical Dermatology ReviewVol. 9(2)
Smt. N.H.L. Municipal Medical College (IN)
Openalex Percentile: Top 90%
Inflammatory Myopathies and Dermatomyositis
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Dermatomyositis: A Multifaceted Autoimmune Connective Tissue Disorder: Series of Seven Cases — Varesh R. Patel, Pooja Agarwal, et al. · Clinical Dermatology Review (2025) | TGRS Research Map | TGRS