Criss-cross heart with complex cardiac malformation, situs inversus totalis and bronchial dysplasia

CCH is a rare congenital heart condition characterized by twisted atrioventricular connections, with complex associated anomalies. Diagnosis is challenging due to the variety of defects. CT angiography is crucial for comprehensive assessment and surgical planning. This case presented a unique combination of CCH with mirror dextrocardia, situs inversus totalis, and bronchial malformation, highlighting the importance of CT in guiding treatment decisions. However, postoperative follow-up is lacking, and optimal surgical strategies for such complex deformities remain to be explored.

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Publication Details

Journal
BMC Cardiovascular Disorders
Published
2025-04-02
DOI
https://doi.org/10.1186/s12872-025-04659-y
Citations
1
Primary Topic
Congenital Heart Disease Studies
Type
article
Field-Weighted Citation Impact
1.35
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article

Criss-cross heart with complex cardiac malformation, situs inversus totalis and bronchial dysplasia

Xiaojuan Ji, Hongqin Liang, Jian Wang, Nan Zhang et al.
1 citations
BMC Cardiovascular Disorders
Congenital Heart Disease Studies
1.35
article

Criss-cross heart with complex cardiac malformation, situs inversus totalis and bronchial dysplasia

Xiaojuan Ji, Hongqin Liang, Jian Wang, Nan Zhang, Li Kong, Fei Liu
article en
1 citations

Abstract

CCH is a rare congenital heart condition characterized by twisted atrioventricular connections, with complex associated anomalies. Diagnosis is challenging due to the variety of defects. CT angiography is crucial for comprehensive assessment and surgical planning. This case presented a unique combination of CCH with mirror dextrocardia, situs inversus totalis, and bronchial malformation, highlighting the importance of CT in guiding treatment decisions. However, postoperative follow-up is lacking, and optimal surgical strategies for such complex deformities remain to be explored.

BMC Cardiovascular DisordersVol. 25(1)
Army Medical University (CN), Chongqing Maternal and Child Health Hospital (CN), Beijing Anzhen Hospital (CN), Southwest Hospital (CN), Second Affiliated Hospital of Nanjing Medical University (CN), Children's Hospital of Chongqing Medical University (CN), Chongqing Medical University (CN)
Openalex Percentile: Top 21%
Congenital Heart Disease Studies
1.35
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Criss-cross heart with complex cardiac malformation, situs inversus totalis and bronchial dysplasia — Xiaojuan Ji, Hongqin Liang, et al. · BMC Cardiovascular Disorders (2025) | TGRS Research Map | TGRS