Phacomatosis cesiomarmorata in a newborn: A case report and review of literature

Phacomatosis pigmentovascularis (PPV) is a congenital disorder with the coexistence of pigmentary nevi and vascular malformation. The disorder can be localized to the skin or accompanied by systemic abnormalities. Phacomatosis cesiomarmorata is one of the subtypes of PPV characterized by Cutis marmorata telangiectatica congenital (CMTC) and nevus cesius. Herein, we describe a case of phacomatosis cesiomarmorata with the nevus cesius and CMTC in a newborn with no systemic abnormalities.