Dermatofibrosarcoma Protuberans of Inguinal Region: A Case Report

Dermatofibrosarcoma is a rare tumour involving the skin. It is a low-grade soft-tissue sarcoma that is commonly seen in middle-aged individuals, usually in the third and fourth decades of life, with males showing a higher prevalence than females. The authors reported a case of a 48-year-old female patient who presented to the hospital with complaints of multiple right inguinal swellings for three months, along with a reported recent increase in size over the last month. On examination, multiple papulomatous lesions, approximately 5×3 cm in size, were observed in the right inguinal region. Ultrasonography (USG) revealed well-defined lesions with a relatively mixed pattern and a few cystic areas noted in the subcutaneous plane, measuring approximately 40×25 mm. These lesions exhibited raised vascularity on colour Doppler imaging. The histopathological examination revealed myxoid tissue showing spindle or satellite cells with oval elongated nuclei and indistinct cytoplasm, suggestive of dermatofibrosarcoma. Dermatofibrosarcoma protuberans is an unusual soft-tissue tumour of the skin, and ultrasonography can significantly help in its diagnosis and management.