Idiopathic Atrophoderma of Pasini and Pierini in a Zosteriform Pattern on Face

Idiopathic atrophoderma of Pasini and Pierini (IAPP) is an uncommon skin condition that affects the organization of dermal collagen resulting in atrophy, evident on histopathological examination. Dermoscopy shows a prominent pigment network with irregular distribution and a storiform pattern. The present report describes a case of a 14-year-old girl who had zosteriform pattern of atrophoderma of Pasini and Pierini on the left side of the face. Histopathology revealed epidermal flattening and decrease in the thickness of the dermis and fragmentation of collagen with mild perivascular and periappendageal, lymphocytic inflammatory infiltrate and confirmed the diagnosis of atrophoderma of Pasini and Pierini. We present this case due to its rarity as zosteriform distribution and age group affected. IAPP is challenging in terms of its etiology and appropriate clinical and histological diagnosis. The therapeutical approach includes topical corticosteroids, antimalarials, and Q-switched Alexandrite laser that have been reported to result in the clinical improvement of hyperpigmented lesions.