Type 2 Congenital Pulmonary Airway Malformation in Tetralogy of Fallot with Absent Pulmonary Valve Syndrome

Tetralogy of Fallot with absent pulmonary valve syndrome is a unique congenital condition often accompanied with dilated pulmonary arteries causing varied degree of airway compression. Frequently, abnormal pulmonary arterial branching at the segmental level and compression at the level of intrapulmonary bronchi can be seen. The occurrence of isolated bronchopulmonary malinosculation in the form of congenital pulmonary airway malformation is exceedingly rare. This report highlights a case of such rarity, involving a young child with recurrent lower respiratory tract infections.