Surgical Repair of the Aorta in a Neonate With Arterial Tortuosity Syndrome
Arterial tortuosity syndrome (ATS) is an autosomal-recessive genetic connective tissue disorder that affects the aorta and medium-sized arterial vessels.<sup>1</sup> We report a case of successful surgical management of the descending aorta in a ten-day-old patient with ATS who presented with multiorganic failure. The aortic reconstruction with a pulmonary homograft patch was performed using full-flow body perfusion.
Authors
- I.A. Soynov (ORCID: https://orcid.org/0000-0003-3691-2848)
- N. R. Nichay (ORCID: https://orcid.org/0000-0002-1763-9535)
- A.N. Аrkhipov (ORCID: https://orcid.org/0000-0003-3234-5436)
- Yu.Yu. Kulyabin (ORCID: https://orcid.org/0000-0002-2361-5847)
- D. Zemel
- Darya A. Dulceva
Institutions
- Meshalkin National Medical Research Center (RU)
Publication Details
- Journal
- World Journal for Pediatric and Congenital Heart Surgery
- Published
- 2025-03-25
- DOI
- https://doi.org/10.1177/21501351251322161
- Primary Topic
- Cardiovascular Issues in Pregnancy
- Type
- article
- Field-Weighted Citation Impact
- 0.00