Improved Chronic Thrombocytopenia After Pulmonary Valve Replacement in a Patient With Shone’s Complex

We report the case of a 21-year-old patient who had long been incorrectly diagnosed as having treatment-resistant idiopathic thrombocytopenic purpura with chronic thrombocytopenia.The patient had Shone's complex and underwent multiple cardiac surgeries including the Ross-Konno procedure in her childhood.At the ages of 12 and 21 years, she underwent pulmonary valve replacement for pulmonary valve deterioration.In her last surgery, a small defect was found between the pulmonary artery and the reconstructed right ventricular outflow tract.A pseudoaneurysm developed because of the small defect, which was successfully repaired.Since then, her thrombocytopenia has improved spontaneously.