Long-Term Clinical Landscapes of Spinal Hypertrophic Pachymeningitis With Anti-Neutrophil Cytoplasmic Antibody–Associated Vasculitis
Our findings highlight the significant pathogenic role of ANCA in spinal HP. MPO-ANCA<sup>+</sup> spinal HP, as an organ-threatening disease, should be positioned as having unique characteristics, whether limited to the CNS or as part of a generalized form in ANCA-associated vasculitis.
Authors
- Kei Watanabe (ORCID: https://orcid.org/0000-0002-1902-0453)
- Hironaka Igarashi (ORCID: https://orcid.org/0000-0003-1663-5564)
- Etsuji Saji (ORCID: https://orcid.org/0000-0003-2743-3175)
- Izumi Kawachi (ORCID: https://orcid.org/0000-0002-7140-8500)
- Mariko Hokari
- Akiyoshi Kakita (ORCID: https://orcid.org/0000-0003-4244-0277)
- Kazuhiro Sanpei
- Yutaka Otsu
- Hiroshi Shimizu (ORCID: https://orcid.org/0000-0002-4869-502X)
- Kaori Yanagawa
- Kouichirou Okamoto (ORCID: https://orcid.org/0000-0001-7737-1596)
- Shunsei Hirohata (ORCID: https://orcid.org/0000-0003-1911-7383)
- Keitaro Minato (ORCID: https://orcid.org/0000-0002-0556-6439)
- Yasuko Toyoshima (ORCID: https://orcid.org/0000-0002-4252-6778)
- Hirotoshi Kikuchi (ORCID: https://orcid.org/0000-0002-1864-1098)
- Mitsunori Yamada
- Hitoshi Takahashi (ORCID: https://orcid.org/0009-0003-4103-0652)
- Aya Nawata (ORCID: https://orcid.org/0000-0002-7871-2425)
- Fumihiro Yanagimura (ORCID: https://orcid.org/0000-0002-8083-4886)
- Osamu Onodera (ORCID: https://orcid.org/0000-0003-3354-5472)
- Daisuke Kobayashi (ORCID: https://orcid.org/0000-0002-0384-8678)
- Masatoyo Nishizawa (ORCID: https://orcid.org/0000-0001-9442-6827)
- Noboru Sato
- Musashi Arakawa
- Kazuaki Awamori
- Akihiro Nakajima
- Akiko Yokoseki
- Takahiro Wakasugi
- Yukiko Nozawa
Institutions
- Tokyo Medical and Dental University (JP)
- Shinshu University (JP)
- University of Occupational and Environmental Health Japan (JP)
- Kaetsu University (JP)
- Nagara Medical Center (JP)
- Niigata City General Hospital (JP)
- Kameda Medical Center (JP)
- Niigata University Medical and Dental Hospital (JP)
- Sado General Hospital (JP)
- Nobuhara Hospital (JP)
- Nishi Niigata Chuo National Hospital (JP)
- Kitasato University (JP)
- Niigata University of Health and Welfare (JP)
- Niigata University (JP)
- Teikyo University (JP)
- Musashi University (JP)
Publication Details
- Journal
- Neurology
- Published
- 2025-03-19
- DOI
- https://doi.org/10.1212/wnl.0000000000213420
- Citations
- 4
- Primary Topic
- IgG4-Related and Inflammatory Diseases
- Type
- article
- Field-Weighted Citation Impact
- 6.67