National Consensus Guideline on Diagnosis and Management of Congenital Neutropenias

At present, a national consensus or guideline for diagnosing and managing patients suspected of having se- vere congenital neutropenia (SCN) is lacking. This consensus is written based on a combination of scientific literature and comments from the expert panel of Iranian immunologists. A group of clinical immunolo- gists reviewed the current consensus, presented their comments at a meeting titled “First Meeting on the Diagnosis of Inborn Errors of Immunity (IEI) by IEI Experts” and agreed on this consensus. This consensus guideline provides recommendations on the diagnosis, antimicrobial prophylaxis, management of clinical manifestations, administration of granulocyte colony-stimulating factor (G-CSF) and hematopoietic stem cell transplantation (HSCT) for patients with SCN.

Authors

Institutions

Publication Details

Journal
Immunology and Genetics Journal
Published
2025-03-16
DOI
https://doi.org/10.18502/igj.v8i3.18171
Primary Topic
Blood disorders and treatments
Type
article
Field-Weighted Citation Impact
0.00
Controls
|||
ALL TIME
JAN
FEB
MAR
APR
MAY
JUN
JUL
AUG
SEP
OCT
article

National Consensus Guideline on Diagnosis and Management of Congenital Neutropenias

Reza Shiari, Taher Cheraghi, Mahnaz Sadeghi‐Shabestari, Sima Bahrami et al.
Immunology and Genetics Journal
Blood disorders and treatments
article

National Consensus Guideline on Diagnosis and Management of Congenital Neutropenias

Reza Shiari, Taher Cheraghi, Mahnaz Sadeghi‐Shabestari, Sima Bahrami, Alireza Shafiei, Golnaz Eslamian, Parisa Ashournia, Reza Yazdani, Majid Marjani, Vahid Ziaee, Mehrnaz Mesdaghi, Narges Eslami, Sepideh Darougar, Maryam Behfar, Saba Fekrvand, Sima Shokri, Aida Askarisarvestani, Shabnam Eskandarzadeh, Mohammamd Nabavi, Anahita Razaghian, Ahmad Vosughimotlagh, Mohammadreza Modaresi, Zahra Daneshmandi, Sarehsadat Ebrahimi, Shaikh Sanjid Seraj, Mahshid Movahedi, Shahrzad Fallah, Samaneh Abdolahzade, Ali Haghbin, Seyedehshabnam Seyedsalehi, Saman Tavakoli
article en

Abstract

At present, a national consensus or guideline for diagnosing and managing patients suspected of having se- vere congenital neutropenia (SCN) is lacking. This consensus is written based on a combination of scientific literature and comments from the expert panel of Iranian immunologists. A group of clinical immunolo- gists reviewed the current consensus, presented their comments at a meeting titled “First Meeting on the Diagnosis of Inborn Errors of Immunity (IEI) by IEI Experts” and agreed on this consensus. This consensus guideline provides recommendations on the diagnosis, antimicrobial prophylaxis, management of clinical manifestations, administration of granulocyte colony-stimulating factor (G-CSF) and hematopoietic stem cell transplantation (HSCT) for patients with SCN.

Immunology and Genetics Journal
Isfahan University of Medical Sciences (IR), Zanjan University of Medical Sciences (IR), Ahvaz Jundishapur University of Medical Sciences (IR), Iran University of Medical Sciences (IR), Tabriz University of Medical Sciences (IR), Shiraz University of Medical Sciences (IR), Guilan University of Medical Sciences (IR), Islamic Azad University Medical Branch of Tehran (IR), Masih Daneshvari Hospital (IR), Rasool Akram Hospital (IR), Children's Medical Center (IR), Stem Cell Technology Research Center (IR), North Khorasan University of Medical Sciences (IR), Shahid Beheshti University (IR), Shahid Beheshti University of Medical Sciences (IR), Tehran University of Medical Sciences (IR)
Openalex Percentile: Top 94%
Blood disorders and treatments
AI Navigator

Ask Laika to Summarize, Analyze, and Connect papers live on the map.

Summarize Papers & Methodologies

Extract key findings, datasets, and comparative methods across publications.

Benchmark Rankings & Visual Analytics

Rank top research institutions, authors, funders, topics, and journals by Field-Weighted Citation Impact (FWCI) and paper volume with instant charts.

Connect Distant Disciplines

Bridge topological clusters on the map to find hidden collaborative intersections.