Anesthetic Management of Inguinal Hernia Surgery in an Adult Patient With Arthrogryposis Multiplex Congenita: A Case Report
Arthrogryposis multiplex congenita (AMC) poses major anesthetic challenges due to severe joint contractures, airway restrictions, and a debated risk of malignant hyperthermia. Despite these complexities, anesthetic reports in adult AMC patients remain extremely limited, leaving perioperative management largely unstandardized. We present the anesthetic approach for a 35-year-old male patient with AMC undergoing open inguinal hernia repair. Given the high risk of airway compromise and joint immobility, we opted for ultrasound-guided ilioinguinal and iliohypogastric nerve blocks with dexmedetomidine sedation, avoiding endotracheal intubation and volatile anesthetics. This case highlights regional anesthesia as a critical alternative to general anesthesia, providing valuable insights into safe, tailored anesthetic strategies for this rare and underreported population.
Authors
- Thalis Asimakopoulos (ORCID: https://orcid.org/0009-0002-7268-3720)
- Irene C Kouroukli
- Panagiotis Prodromakis
Institutions
- Hippocration General Hospital (GR)
Publication Details
- Journal
- Cureus
- Published
- 2025-03-09
- DOI
- https://doi.org/10.7759/cureus.80300
- Primary Topic
- Neurogenetic and Muscular Disorders Research
- Type
- article
- Field-Weighted Citation Impact
- 0.00