Osteoma cutis

In this report, we discuss two children with progressive cutaneous ossification and review its aetiology and associations. Osteoma cutis (OC) is a cutaneous disease associated with ossification in the dermis or subcutaneous tissue, classified as either primary or secondary. Primary OC is rare. Although it can occur <i>de novo</i>, it has significant genetic and metabolic associations that must be excluded and warrants a thorough clinical workup. Secondary OC arises in response to inflammation, neoplasia or trauma and may have aesthetic concerns.