GRAND ROUNDS: A 29-year-old woman with right lower lid mass

Extraosseous Ewing sarcoma is a rare entity mostly seen in the extremities and chest cavity in older individuals. Although osseous orbital Ewing sarcoma has been reported, extraosseous orbital involvement is extremely rare. We report the case of a young woman who presented with lower eyelid mass lesion. The results of histopathological and immunohistochemical analysis were suggestive of Ewing sarcoma. Radiological imaging and a PET-CT ruled out any bony orbital or systemic involvement. The patient was started on a standard chemotherapeutic protocol for Ewing sarcoma.