Cardiac magnetic resonance imaging in the follow-up of patients with Fabry cardiomyopathy
Variations in native myocardial T1 values at cardiac MRI are significantly greater in patients with Fabry disease receiving treatment than in untreated patients, suggesting an effect of treatment on lipid storage. In addition, changes in T2 values suggest an anti-inflammatory effect of the treatment.
Authors
- Olivier Ghekiere (ORCID: https://orcid.org/0000-0002-9229-9489)
- Soraya El Ghannudi (ORCID: https://orcid.org/0000-0002-3706-8039)
- Sébastien Normant
- Jean‐Nicolas Dacher
- Farah Cadour (ORCID: https://orcid.org/0000-0001-5525-0304)
- Julien Burel (ORCID: https://orcid.org/0000-0001-8726-265X)
- Olivier Lairez (ORCID: https://orcid.org/0000-0001-8141-6582)
- Fabien Labombarda (ORCID: https://orcid.org/0000-0003-4435-4401)
- Alexis Jacquier (ORCID: https://orcid.org/0000-0003-0297-7942)
- Jules Senlis
- Matthieu Demeyere
- Arthur Flouriot
Institutions
- Inserm (FR)
- Centre Hospitalier Universitaire de Toulouse (FR)
- Assistance Publique Hôpitaux de Marseille (FR)
- Normandie Université (FR)
- Centre Hospitalier Universitaire de Caen Normandie (FR)
- Centre Hospitalier Universitaire de Rouen (FR)
- Hôpital de la Timone (FR)
- Hôpital Civil, Strasbourg (FR)
- Université de Rouen Normandie (FR)
- Université de Strasbourg (FR)
- Hasselt University (BE)
- Université de Caen Normandie (FR)
Publication Details
- Journal
- Diagnostic and Interventional Imaging
- Published
- 2025-02-23
- DOI
- https://doi.org/10.1016/j.diii.2025.02.002
- Citations
- 1
- Primary Topic
- Lysosomal Storage Disorders Research
- Type
- article
- Field-Weighted Citation Impact
- 1.16
Funders
- Takeda Pharmaceuticals International