Independent External Evaluation of Pediatric Hypertrophic Cardiomyopathy Risk Scores in Predicting Severe Ventricular Arrhythmias
In this independent evaluation, our findings suggest imperfect discrimination between low and high-risk patients using the HCM Risk-Kids and PRIMaCY risk scores, with predicted risks tending to be overestimated compared with the actual observed events. The performance or risk scores was substantially improved by periodic reassessment during follow-up.
Authors
- Éloi Marijon (ORCID: https://orcid.org/0000-0001-7227-3428)
- Marie Wilkin (ORCID: https://orcid.org/0000-0001-8680-1092)
- Victor Waldmann (ORCID: https://orcid.org/0000-0001-8057-1900)
- Olivier Raisky
- Damien Bonnet (ORCID: https://orcid.org/0000-0002-8722-5805)
- Margaux Pontailler (ORCID: https://orcid.org/0000-0001-9375-2444)
- Elena Panaioli (ORCID: https://orcid.org/0000-0002-3668-0445)
- Diala Khraiche (ORCID: https://orcid.org/0000-0002-3437-9333)
Institutions
- Inserm (FR)
- Université Paris Cité (FR)
- Institut Necker Enfants Malades (FR)
- Sorbonne Paris Cité (FR)
- Hôpital Européen Georges-Pompidou (FR)
- Paris Cardiovascular Research Center (FR)
- European Hospital (IT)
Publication Details
- Journal
- Circulation Arrhythmia and Electrophysiology
- Published
- 2025-02-20
- DOI
- https://doi.org/10.1161/circep.124.012932
- Citations
- 2
- Primary Topic
- Cardiomyopathy and Myosin Studies
- Type
- article
- Field-Weighted Citation Impact
- 2.78