Aneurysm and subacute type a aortic dissection, in a pediatric patient with aortopathy

Aortic dissection in pediatrics is an extremely rare condition, which is generally related to predisposing factors such as connective tissue disorders, congenital heart disease and systemic arterial hypertension. A 3-year-old girl, with a history of bicuspid aortic valve, hypoplasia of the aortic arch and repaired aortic coarctation at one month of age. She was admitted 2 months of atypical chest pain, dysphonia, and low tone of voice. The echocardiogram and CT angiography showed an image corresponding to a Stanford A aortic dissection, with false lumen perfusion that generated a aneurysmal dilation with a saccular morphology of 53 × 40 × 70 mm dimensions. The patient was taken to surgery, exposure of the ascending aorta, aneurysmal dissection, and replacement with a 22 mm supracoronary tube were performed. We present a case of a 3-year-old pediatric patient with Stanford A aortic dissection, subacute evolution, with successful repair.