RVOT Stenting in a Child With Tetralogy of Fallot and Hypertrophic Cardiomyopathy
The coexistence of Tetralogy of Fallot (TOF) and hypertrophic cardiomyopathy (HCM) is extremely rare and poses significant clinical challenges. We present a case that highlights the management strategy for this complex condition. A 3-year-old boy presented with recurrent cyanotic spells, leading to a diagnosis of TOF complicated by HCM. Right ventricular outflow tract stenting (RVOTS) was performed to stabilize the patient. The combination of TOF and HCM is associated with a high mortality rate and the management strategy is not standardized. In this case, RVOTS was done, resulting in a favorable immediate response and short-term outcome. This represents the first documented use of RVOTS in a patient with TOF and HCM. The combination of TOF and HCM is a rare and complex clinical entity. RVOTS has demonstrated effectiveness as a palliative strategy, leading to positive immediate and short-term outcomes in this unique case.
Authors
- Mohammad Azam Haseen
- Shamayal Rabbani
- Mohammad Moaaz Kidwai
- Shaad Abqari
Institutions
- Jawaharlal Nehru Medical College Hospital (IN)
Publication Details
- Journal
- JACC Case Reports
- Published
- 2025-02-01
- DOI
- https://doi.org/10.1016/j.jaccas.2024.102969
- Primary Topic
- Congenital Heart Disease Studies
- Type
- article
- Field-Weighted Citation Impact
- 0.00