Right atrial strain in Anderson–Fabry disease
In FD impaired RA strain is a common finding. RA reservoir and contractile strains are reduced in FD patients even before LVH ensues, as compared to controls. LA reservoir strain and LV-GLS show an independent correlation with RA reservoir strain.
Authors
- Francesca Graziani (ORCID: https://orcid.org/0000-0002-4520-5689)
- Maria Chiara Meucci (ORCID: https://orcid.org/0000-0001-5474-0555)
- Gaetano Antonio Lanza (ORCID: https://orcid.org/0000-0003-2187-6653)
- Giulia Iannaccone (ORCID: https://orcid.org/0000-0002-7483-7781)
- Antonella Lombardo (ORCID: https://orcid.org/0000-0003-3162-1830)
- Rosa E. Lillo (ORCID: https://orcid.org/0000-0003-0802-4691)
- Mario Marsilia
- Filippo Tusa
- Alessio Cianci (ORCID: https://orcid.org/0009-0007-4520-2318)
- Francesco Burzotta (ORCID: https://orcid.org/0000-0002-6569-9401)
- Claudio Di Brango
Institutions
- Università Cattolica del Sacro Cuore (IT)
- Agostino Gemelli University Polyclinic (IT)
- Istituti di Ricovero e Cura a Carattere Scientifico (IT)
Publication Details
- Journal
- Frontiers in Cardiovascular Medicine
- Published
- 2025-02-18
- DOI
- https://doi.org/10.3389/fcvm.2025.1496534
- Primary Topic
- RNA regulation and disease
- Type
- article
- Field-Weighted Citation Impact
- 0.00