Congenital Absence of Portal Vein Presenting With Hematemesis in a Young Patient

Upper gastrointestinal bleeding is caused by multiple different etiologies, with one being portal hypertension. Identifying the underlying cause of portal hypertension is extremely important in determining further management. This is a rare case of a patient who had developed portal hypertension secondary to a congenital absence of a portal vein with no other medical history. This case highlights a rare cause of portal hypertension and the need for prompt medical management.