Anaesthetic management of a rare case of congenital factor VII deficiency – Patient posted for shoulder arthroscopic synovectomy: A case report

Factor VII deficiency (F7D) is a rare coagulation disorder. It poses significant challenges for anaesthetic management due to a heightened risk of bleeding. This case report describes the successful anaesthetic management of a 20-year-old woman with congenital F7D who underwent elective shoulder arthroplasty for ‘Pigmented Villonodular Synovitis.’ A multidisciplinary approach incorporating preoperative recombinant activated factor VII and tranexamic acid, general anaesthesia with an interscalene brachial block, and meticulous surgical technique and close monitoring ensured a favourable outcome. This approach emphasises the importance of early identification and meticulous management of F7D to ensure safe surgical outcomes.