Idiopathic lobular panniculitis. Clinical case

Panniculitis includes heterogeneous diseases characterized by an immuno-inflammatory process in the subcutaneous fat. Often the musculoskeletal system and internal organs are involved in the pathological process. The etiology and pathogenesis of panniculitis are not fully understood, however, the immunopathological nature of the disease is most likely. There is no uniform classification of panniculitis. Ideopathic lobular panniculitis (ILP) (synonyms: recurrent febrile non-suppurating panniculitis, nodular Pfeiffer-Weber-Christian panniculitis) is of particular clinical interest. ILP according to ICD-10 refers to systemic connective tissue lesions (M 35.6). The described clinical case of IPD demonstrates the difficulty of diagnosing this disease.

Authors

Publication Details

Journal
Clinical review for general practice
Published
2024-10-26
DOI
https://doi.org/10.47407/kr2024.5.10.00492
Primary Topic
Autoimmune Bullous Skin Diseases
Type
article
Field-Weighted Citation Impact
0.00
Controls
|||
ALL TIME
JAN
FEB
MAR
APR
MAY
JUN
JUL
AUG
SEP
OCT
article

Idiopathic lobular panniculitis. Clinical case

N. V. Ovsyannikov, Olga V. Zamakhina, Dmitrij R. Mingulov, Vladimir F. Gorshkov et al.
Clinical review for general practice
Autoimmune Bullous Skin Diseases
article

Idiopathic lobular panniculitis. Clinical case

N. V. Ovsyannikov, Olga V. Zamakhina, Dmitrij R. Mingulov, Vladimir F. Gorshkov, Vitalij V. Klishin
article en

Abstract

Panniculitis includes heterogeneous diseases characterized by an immuno-inflammatory process in the subcutaneous fat. Often the musculoskeletal system and internal organs are involved in the pathological process. The etiology and pathogenesis of panniculitis are not fully understood, however, the immunopathological nature of the disease is most likely. There is no uniform classification of panniculitis. Ideopathic lobular panniculitis (ILP) (synonyms: recurrent febrile non-suppurating panniculitis, nodular Pfeiffer-Weber-Christian panniculitis) is of particular clinical interest. ILP according to ICD-10 refers to systemic connective tissue lesions (M 35.6). The described clinical case of IPD demonstrates the difficulty of diagnosing this disease.

Clinical review for general practiceVol. 5(10)
Openalex Percentile: Top 59%
Autoimmune Bullous Skin Diseases
AI Navigator

Ask Laika to Summarize, Analyze, and Connect papers live on the map.

Summarize Papers & Methodologies

Extract key findings, datasets, and comparative methods across publications.

Benchmark Rankings & Visual Analytics

Rank top research institutions, authors, funders, topics, and journals by Field-Weighted Citation Impact (FWCI) and paper volume with instant charts.

Connect Distant Disciplines

Bridge topological clusters on the map to find hidden collaborative intersections.