Adenoid Cystic Carcinoma of Sphenoid Sinus: Case Report of a Rare Entity

Adenoid Cystic Carcinoma (ACC) is a rare malignant neoplasm accounting for 1% cases of Head and Neck cancers [1].Primarily a tumour of minor salivary glands, very rarely it is reported as a primary tumour in sinonasal tract where it shows more aggressive pattern of growth as compared to its salivary gland counterparts [1].Its tendency for slow growth and indolent course usually leads to a delayed diagnosis.At the same time, its locally aggressive nature along with proximity to vital structures such as brain and a high propensity for perineural invasion limits the extent of complete surgical management and hence leads to a higher incidence of local recurrence and delayed distant metastasis [2][3][4].Surgery, along with adjuvant radiotherapy, remains the mainstay of treatment depending upon the stage of tumour [3,4].Here, we present a rare case of ACC arising from the sphenoid sinus in a 70-year-old female with isolated symptom of epistaxis resulting in a delayed diagnosis.