Intraocular Myxo-Papillary Ependymoma versus Retinal Gliosis Mimicking Uveal Melanoma: Report of 2 Adult Patients with Clinical, Imaging, and Histopathologic Features
Intraocular ependymoma is a rare intraocular primary retinal tumor which can mimic uveal melanoma at ocular fundus examination and imaging. The diagnosis requires histopathology after enucleation, and can mimic reactive retinal gliosis, whether ependymomas can arise from retina or if retinal gliosis can have ependymoma characteristics is still to be determined. Survival and metastatic prognosis after surgery are favorable according to our experience and previously published cases, confirming the presumed benign nature of the lesions.
Authors
- Arnaud Gauthier (ORCID: https://orcid.org/0000-0003-3096-6204)
- Nathalie Cassoux (ORCID: https://orcid.org/0000-0002-5535-9649)
- Hervé J. Brisse (ORCID: https://orcid.org/0000-0003-2794-5875)
- Alexandre Matet (ORCID: https://orcid.org/0000-0002-9721-777X)
- Ysé Borella
- Julien Masliah‐Planchon (ORCID: https://orcid.org/0000-0002-5596-3926)
- Arnault Tauziède‐Espariat (ORCID: https://orcid.org/0000-0002-9795-5828)
- Livia Lumbroso-Le Rouic
Institutions
- Inserm (FR)
- Université Paris Cité (FR)
- Institut de Psychiatrie et Neurosciences de Paris (FR)
- Institut Curie (FR)
Publication Details
- Journal
- Ocular Oncology and Pathology
- Published
- 2025-02-11
- DOI
- https://doi.org/10.1159/000541778
- Primary Topic
- Ocular Oncology and Treatments
- Type
- article
- Field-Weighted Citation Impact
- 0.00