Facial port wine stain with predominant ipsilateral and islands of contralateral oral mucosal involvement: A rare case report

Nevus Flammeus often referred to as PWS (Portwine stain) are benign capillary malformation characterized by multiple dilated vessels in dermis which progressively becomes ectatic as age advances. Portwine stains presents at birth and clinically manifests as flat bright pink, red or violaceous macules that commonly affects the face but can involve other body parts. Over a period of time these lesions become more darker, thicker and nodular often referred to as cobblestoning. Soft tissue hypertrophy of the adjacent areas is also observed especially for facial lesions. The characteristic dermoscopic features are varying morphology of vascular channels like linear, reticular, sausage like, dots or globules and mixed vessels. Mucosal staining is a typical characteristic of facial PWS. This case is reported for its unique variation of facial portwine stain with predominantly ipsilateral oral mucosal involvement with contralateral red macular islands rarely reported in literature with the aforementioned secondary skin changes and typical dermoscopic features.