Chylothorax and Chylopericardium Complicating Behcet's Disease: A Case Report Hanaa Harraz, Afaf Amir, Nahid Zaghba, Hanane Benjelloun, Khadija Chaanoun, Najiba Yassine Published: Feb. 4, 2025 | 30 19 DOI: https://doi.org/10.36347/sjmcr.2025.v13i02.0

Behçet's disease is a complex multisystem vasculitis of unknown aetiology, characterised by different clinical manifestations and the occurrence of successive attacks interspersed with remissions. Mediastino-pulmonary involvement is rare but severe, resulting mainly in thrombosis of the superior vena cava and pulmonary artery aneurysm. The association between Behçet's disease and chylothorax and/or chylopericardium is rare, with a few cases reported in the literature. We present a case of chylothorax and chylopericardium with thrombosis of the superior vena cava as clinical manifestations in a patient with Behçet's disease. Management was multidisciplinary, based on pleuropericardial drainage, immunosuppressants, anticoagulants and nutritional management.