Extranodal natural killer/T-cell lymphoma with secondary haemophagocytic lymphohistiocytosis simulating orbital inflammatory disease
This case report describes an uncommon case of periorbital swelling due to a rare neoplastic condition, a natural killer/T-cell lymphoma, which presented a significant diagnostic challenge. The malignancy was complicated by hemophagocytic lymphohistiocytosis that led to mortality within a month of initial presentation.
Authors
- Adam Gajdatsy
- Jackson Chee Chea Lee (ORCID: https://orcid.org/0000-0002-7314-0384)
- Nima Mesbah Ardakani (ORCID: https://orcid.org/0000-0001-9477-8291)
- Verity Grace Moynihan
Institutions
- Lions Eye Institute (AU)
- Sir Charles Gairdner Hospital (AU)
- North Metropolitan Health Service (AU)
Publication Details
- Journal
- BMJ Case Reports
- Published
- 2025-02-01
- DOI
- https://doi.org/10.1136/bcr-2024-259848
- Primary Topic
- Autoimmune and Inflammatory Disorders Research
- Type
- article
- Field-Weighted Citation Impact
- 0.00