Littoral cell angioma of the spleen in a 70-year-old male patient with myelodysplastic syndrome: a case report

Introduction: Littoral cell angioma (LCA) is a new subtype of vascular tumor, which has been reported infrequently worldwide.It is associated with visceral malignancies and other immunologic conditions.Clinical case: We present a case of a 70-yearold Caucasian male with a 6-year history of myelodysplastic syndrome, which was investigated for splenomegaly and pancytopenia.Radiological and histopathological examinations revealed an LCA and an open splenectomy were performed.The patient had an uneventful post-operative recovery.Conclusion: LCA is a rare tumor, with atypical presentation often associated with other malignancies or immunologic conditions.Diagnosis is challenging, and so far, splenectomy is the gold standard treatment.