Primary Intra-Thoracic Evans Tumor in A Young Female: Case Report and Literature Review

Evans tumor, also known as low-grade fibromyxoid sarcoma, usually presents as a slowly growing, painless mass in young adults, most commonly involving the proximal extremities.Involvement of the intrathoracic compartment has been rarely described, most often as a site of metastasis.Primary intrathoracic low-grade fibromyxoid sarcoma of the pleura is even rarer.Here, we describe a case report of a young lady with a history of psoriatic arthritis who initially presented with shortness of breath due to left pleural effusion.Further workup revealed a primary intrathoracic low-grade fibromyxoid sarcoma of the left pleura.