Systemic Inflammatory Diseases in Children With Sickle Cell Disease: A French Multicenter Observational Study on Diagnostic and Therapeutic Issues

Delayed diagnosis was frequent due to overlapping clinical presentations between SCD and SID. Clinicians must be aware of warning signs associated with elevated inflammatory markers, hypergammaglobulinemia, or specific antibodies. Therapeutic strategies remain challenging.

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Publication Details

Journal
Pediatric Blood & Cancer
Published
2025-01-27
DOI
https://doi.org/10.1002/pbc.31563
Citations
2
Primary Topic
Hemoglobinopathies and Related Disorders
Type
article
Field-Weighted Citation Impact
3.25
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article

Systemic Inflammatory Diseases in Children With Sickle Cell Disease: A French Multicenter Observational Study on Diagnostic and Therapeutic Issues

Mariane De Montalembert, Corinne Guitton, Isabelle Melki, Loïc de Pontual et al.
2 citations
Pediatric Blood & Cancer
Hemoglobinopathies and Related Disorders
3.25
article

Systemic Inflammatory Diseases in Children With Sickle Cell Disease: A French Multicenter Observational Study on Diagnostic and Therapeutic Issues

Mariane De Montalembert, Corinne Guitton, Isabelle Melki, Loïc de Pontual, Patricia Benhaim, Oussama Charara, Cécile Arnaud, Brigitte Bader‐Meunier, Véronique Hentgen, Annie Kamden, Caroline Vinit, Coralie Bloch‐Queyrat, Florence Missud, Pierre Quartier, Ulrich Meinzer, Vincent Gajdos, Isabelle Kone‐Paut, Sylvie Nathanson, Luu‐Ly Pham, Lahoueri Amor‐Chelihi
article en
2 citations

Abstract

Delayed diagnosis was frequent due to overlapping clinical presentations between SCD and SID. Clinicians must be aware of warning signs associated with elevated inflammatory markers, hypergammaglobulinemia, or specific antibodies. Therapeutic strategies remain challenging.

Pediatric Blood & CancerVol. 72(4)
Hôpital Necker-Enfants Malades (FR), Inserm (FR), Université Paris-Seine (FR), Université Sorbonne Paris Nord (FR), Laboratory of Excellence GR-Ex (FR), Assistance Publique – Hôpitaux de Paris (FR), Hôpital Robert-Debré (FR), Hôpital Jean-Verdier (FR), Hôpital Antoine-Béclère (FR), Centre Hospitalier de Versailles (FR), Hôpital Intercommunal de Créteil (FR), Bicêtre Hospital (FR), Institut des Maladies Génétiques Imagine (FR)
Good health and well-being
Openalex Percentile: Top 11%
Hemoglobinopathies and Related Disorders
3.25
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