Trans-labyrinthine approach for a huge vestibular schwannoma in a patient with neurofibromatosis 2: our experience

Vestibular schwannoma is a schwann cell-derived tumour arising from the vestibulocochlear nerve. These tumours represent 85% of intracranial growths arising at the cerebellopontine angle 1. Various surgical techniques exist for removing it, the most common of which are trans-labyrinthine and retro-sigmoid approaches. The common presenting symptoms include progressive hearing loss and tinnitus which are reported in over 60% of patients. Larger tumours can cause hydrocephalus and brainstem compression leading to symptoms such as facial paraesthesia, vertigo and headache. Here were present a 25 year old male with neurofibromatosis 2 with a huge 4.5 cm vestibular schwannoma successfully removed using trans-labyrinthine approach in our hospital.