WCN25-3512 A RARE CASE OF ROSAI DORFMAN DESTOMBES DISEASE PRESENTING WITH LUPUS NEPHRITIS AND CNS SMALL VESSEL VASCULITIS
Rosai-Dorfman-Destombes (RDD) disease is a rare non-Langerhans cell histiocytosis characterized by tissue accumulation of histiocytes commonly seen in children and young adults. RDD can occur as an isolated disorder or in association with autoimmune and malignant diseases. Steroids, immunomodulators and surgical excision can be used in management of RDD.
Authors
- Prateek kumar Panda
- Sharon Kandari (ORCID: https://orcid.org/0000-0002-5411-5837)
- Arvind Kumar (ORCID: https://orcid.org/0000-0002-9229-1081)
- Arshdeep Singh (ORCID: https://orcid.org/0009-0005-4183-2764)
- Anshuman Biswal
- Rohit Puri
Institutions
- Seema Dental College and Hospital (IN)
- All India Institute of Medical Sciences Rishikesh (IN)
Publication Details
- Journal
- Kidney International Reports
- Published
- 2025-01-27
- DOI
- https://doi.org/10.1016/j.ekir.2024.11.428
- Primary Topic
- Histiocytic Disorders and Treatments
- Type
- article
- Field-Weighted Citation Impact
- 0.00