Esophageal Atresia of Kluth Type-13: Management of a Rare Variant

A full-term low birth-weight female newborn presented with clinical features of esophageal atresia. Investigations revealed Kluth type-13, an extremely rare varient of esophageal atresia without fistula, in which the upper pouch is long and ends blindly just above the diaphragm near the gastro-esophageal junction. She was managed with esophagostomy and feeding gastrostomy in the neonatal period, followed by gastric tube esophagoplasty at 2 years of age. At 18 months of follow-up she is thriving well and asymptomatic.