Incidence of idiopathic syrinx in pediatric patients diagnosed with VACTERL association
Although limited, current estimates suggest the general incidence of an idiopathic syrinx is between 5.6 and 8.4 per 100,000 people; these findings in a pediatric cohort with VACTERL association suggest an incidence of 2200 per 100,000 (i.e., 2.2%). Thus, an idiopathic syrinx may be 200-400 times as prevalent in the pediatric VACTERL population.
Authors
- Daniel Weber (ORCID: https://orcid.org/0000-0003-2567-6317)
- Joanna E. Papadakis (ORCID: https://orcid.org/0000-0002-3058-3513)
- John S. Albanese (ORCID: https://orcid.org/0000-0002-6131-2230)
- Benjamin C. Warf (ORCID: https://orcid.org/0000-0001-6376-4751)
- Ashley K. Birch
Institutions
- Boston Children's Hospital (US)
Publication Details
- Journal
- Journal of Neurosurgery Pediatrics
- Published
- 2025-01-10
- DOI
- https://doi.org/10.3171/2024.10.peds24242
- Primary Topic
- Esophageal and GI Pathology
- Type
- article
- Field-Weighted Citation Impact
- 0.00