Liver Transplant From a Deceased Donor With Cystinosis: A Case Report

Many inherited metabolic disorders (IMD) are associated with end-organ damage necessitating organ transplantation. Although utilization of deceased donors with history of IMD warrants caution, there may be circumstances under which such donors could be considered as suitable organ donor candidates. We present the first known report of liver transplantation from a deceased donor with cystinosis. The donor was a 20-year-old male with infantile cystinosis who had previously undergone two deceased donor kidney transplants. Unfortunately, he incurred cranial trauma, and after careful consideration of the metabolic consequences, his liver was deemed suitable for transplantation. The liver was successfully transplanted into a 65-year-old female recipient with hepatitis C (HCV) cirrhosis. The recipient is currently 12 months post-transplant and experiencing good graft function without evidence of cystine crystals on liver biopsy. This case highlights that liver transplantation from donors with rare IMD can result in favorable outcomes. However, it is crucial to approach the use of such livers with caution. These transplants should be considered after a thorough assessment, ensuring that a comprehensive decision-making process is in place to mitigate potential risks.

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Publication Details

Journal
JIMD Reports
Published
2025-01-01
DOI
https://doi.org/10.1002/jmd2.12467
Primary Topic
Biomedical Research and Pathophysiology
Type
article
Field-Weighted Citation Impact
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article

Liver Transplant From a Deceased Donor With Cystinosis: A Case Report

Matthew H. Levine, Sandra L. Amaral, Samir Abu‐Gazala, Raeda Taj et al.
JIMD Reports
Biomedical Research and Pathophysiology
article

Liver Transplant From a Deceased Donor With Cystinosis: A Case Report

Matthew H. Levine, Sandra L. Amaral, Samir Abu‐Gazala, Raeda Taj, Maarouf Hoteit, Sanmati Cuddapah, Emma E. Furth, Melissa Bleicher, Kim M. Olthoff, Raghuram Reddy, Peter L. Abt, Eyob Feyssa, Elizabeth B. Rand, Kim T. Ng, Frederick Vyas
article en

Abstract

Many inherited metabolic disorders (IMD) are associated with end-organ damage necessitating organ transplantation. Although utilization of deceased donors with history of IMD warrants caution, there may be circumstances under which such donors could be considered as suitable organ donor candidates. We present the first known report of liver transplantation from a deceased donor with cystinosis. The donor was a 20-year-old male with infantile cystinosis who had previously undergone two deceased donor kidney transplants. Unfortunately, he incurred cranial trauma, and after careful consideration of the metabolic consequences, his liver was deemed suitable for transplantation. The liver was successfully transplanted into a 65-year-old female recipient with hepatitis C (HCV) cirrhosis. The recipient is currently 12 months post-transplant and experiencing good graft function without evidence of cystine crystals on liver biopsy. This case highlights that liver transplantation from donors with rare IMD can result in favorable outcomes. However, it is crucial to approach the use of such livers with caution. These transplants should be considered after a thorough assessment, ensuring that a comprehensive decision-making process is in place to mitigate potential risks.

JIMD ReportsVol. 66(1)
Children's Hospital of Philadelphia (US), Hospital of the University of Pennsylvania (US), University of Pennsylvania (US)
Good health and well-being
Openalex Percentile: Top 99%
Biomedical Research and Pathophysiology
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