Retroperitoneal Müllerian cyst causing uterine protrusion in a teenage girl

Retroperitoneal Müllerian cysts, though rare, should be considered in differential diagnoses of retroperitoneal cystic tumors, especially in patients with associated urogenital anomalies. Immunohistochemical profiling plays a critical role in distinguishing Müllerian cysts from other urogenital cysts. Patients with renal anomalies should be evaluated for associated urogenital anomalies, and surgical intervention should be considered based on symptom presentation and potential for malignancy.