Chronic vegetative eruption in a child

Pyodermatitis-pyostomatitis vegetans (PD-PSV) is a rarely described benign inflammatory skin disease of unknown etiology. It is often associated with chronic inflammatory bowel disease. It is common in young and middle-aged individuals, yet rarely in children. Herein, we report the case of a young child who had developed pustular lesions on the skin and mouth as a manifestation of PD-PSV with manifestations associated with primary immune deficiency (PID). Treatment with immunoglobulins and antimycotics resulted in the resolution of the cutaneous and mucosal lesions. To our knowledge, the association between PD-PSV and DIP has not been previously reported. Key words: pyodermatitis, Pyostomatitis, Primary immune deficiency, Pyodermatitis-pyostomatitis vegetans