Panniculitis in Anti-MDA-5 Positive Juvenile Dermatomyositis: A Case Report
Panniculitis is a rare clinical finding in dermatomyositis. There are few reported cases in the medical literature. In this report, we describe a 17-year-old male patient with anti-MDA5 positive hypomyopathic dermatomyositis who, eight months after diagnosis, presented with indurated nodules on the right forearm and right thigh despite methotrexate and monthly intravenous immunoglobulin treatment. A skin biopsy revealed lobular panniculitis with lymphocytic infiltrate. His lesions were successfully controlled with hydroxychloroquine and azathioprine. This article presents a case regarding the rarity of panniculitis in juvenile dermatomyositis and its treatment strategy.
Authors
- Erdem Çomut (ORCID: https://orcid.org/0000-0002-3386-4206)
- Selçuk Yüksel (ORCID: https://orcid.org/0000-0001-9415-1640)
- Gülşah Kılbaş (ORCID: https://orcid.org/0000-0001-5932-1990)
- Semra Ayduran (ORCID: https://orcid.org/0000-0002-6183-0935)
- Serkan Türkuçar (ORCID: https://orcid.org/0000-0003-4700-1361)
- Saadet Nilay Tığrak (ORCID: https://orcid.org/0000-0003-0381-6040)
Institutions
- Çanakkale Onsekiz Mart Üniversitesi (TR)
- Pamukkale University (TR)
Publication Details
- Journal
- Journal of Nepal Medical Association
- Published
- 2024-12-31
- DOI
- https://doi.org/10.31729/jnma.8874
- Primary Topic
- Inflammatory Myopathies and Dermatomyositis
- Type
- article
- Field-Weighted Citation Impact
- 0.00