Dedifferentiated Liposarcoma of Kidney: A Rare Entity

Liposarcoma is an uncommon mesenchymal tumor. There are several histological variants. Dedifferentiated liposarcoma is often located retroperitoneally. Renal localization is exceptional. In this article, we report a case of primary renal dedifferentiated liposarcoma treated by radical total nephrectomy. Imaging assessment suspected a malignant tumor. It was the histological examination with an immunohistochemical complement that confirmed the diagnosis of dedifferentiated renal liposarcoma. The prognosis remains poor.