Epidemiological and clinicopathological characteristics of vascular-limited renal AL amyloidosis

Renal vascular-limited AL amyloidosis is a probably underdiagnosed disease with markedly reduced eGFR, low-grade proteinuria and severe overall prognosis. Rapid achievement of a deep hematological response is required to preserve long-term renal and patient outcomes.

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Publication Details

Journal
Nephrology Dialysis Transplantation
Published
2024-12-12
DOI
https://doi.org/10.1093/ndt/gfae285
Citations
3
Primary Topic
Amyloidosis: Diagnosis, Treatment, Outcomes
Type
article
Field-Weighted Citation Impact
0.70
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article

Epidemiological and clinicopathological characteristics of vascular-limited renal AL amyloidosis

Emmanuel Estève, Jérôme Olagne, Nathanaël Beeker, Hélène Perrochia et al.
3 citations
Nephrology Dialysis Transplantation
Amyloidosis: Diagnosis, Treatment, Outcomes
0.70
article

Epidemiological and clinicopathological characteristics of vascular-limited renal AL amyloidosis

Emmanuel Estève, Jérôme Olagne, Nathanaël Beeker, Hélène Perrochia, Kathleen Dessaix, Magali Colombat, Elsa Ferrière, Benjamin Carpentier, Nicolas Wayolle, Mathieu Wémeau, Pierre Pinson, Marion Rabant, Frank Bridoux, Camille Cohen, Noémie Senot, Jean Michel Goujon, Jean Baptiste Gibier
article en
3 citations

Abstract

Renal vascular-limited AL amyloidosis is a probably underdiagnosed disease with markedly reduced eGFR, low-grade proteinuria and severe overall prognosis. Rapid achievement of a deep hematological response is required to preserve long-term renal and patient outcomes.

Nephrology Dialysis TransplantationVol. 40(7)
Hôpital Necker-Enfants Malades (FR), Inserm (FR), Université Paris Cité (FR), Centre Hospitalier Universitaire de Lille (FR), Sorbonne Université (FR), Centre Hospitalier de Roubaix (FR), Hôpital Cochin (FR), Centre Hospitalier Universitaire de Montpellier (FR), Assistance Publique – Hôpitaux de Paris (FR), Institut universitaire du cancer de Toulouse Oncopole (FR), Toulouse Mathematics Institute (FR), Hôpital Européen Georges-Pompidou (FR), Hôpital Européen (FR), Centre Hospitalier Universitaire de Poitiers (FR), Centre de Recherche sur l'Inflammation (FR), Centre Hospitalier de Béthune (FR), Hôpital Bichat-Claude-Bernard (FR), Hôpital Saint-Vincent-de-Paul (FR), Hôpital Tenon (FR), Maladies rénales fréquentes et rares : des mécanismes moléculaires à la médecine personnalisée, Université de Strasbourg (FR)
Good health and well-being
Openalex Percentile: Top 28%
Amyloidosis: Diagnosis, Treatment, Outcomes
0.70
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