Rectal clear cell carcinoma of Mullerian origin

Clear cell carcinoma is a malignant tumor arising from paramesonephric ducts such as kidneys, ovaries, cervix and vagina. There are two types of clear cell carcinoma, intestinal and Mullerian type. Primary clear cell carcinoma of rectum is a rare entity. Extra Mullerian involvement of clear cell carcinoma of Mullerian type arises exclusively in the rectum or sigmoid of women. There are case reports of clear cell carcinoma of Mullerian origin arising in endometriosis in multiple sites. We report a case of clear cell carcinoma of Mullerian type in rectum in 63 year old female with no evidence of endometriosis.