Oral management of Allgrove Syndrome: a case report

Allgrove Syndrome, also known as Triple A syndrome, is a rare autosomal recessive disorder characterized by the triad of achalasia, alacrima, and adrenal insufficiency. First described in 1978, the etiology of this syndrome remains unclear, and its prevalence is unknown, with fewer than a hundred cases reported in the literature. The syndrome exhibits significant variability in its clinical presentation, even among individuals within the same family, making both diagnosis and management particularly challenging. The aim of this study was to report the oral management of a twenty-one-year-old woman diagnosed with Allgrove Syndrome, emphasizing the unique challenges posed by this condition due to the multisystem involvement associated with the disorder. Managing the oral health of patients with Allgrove Syndrome requires meticulous consideration of their complex medical history, especially the presence of adrenal insufficiency. This condition necessitates specific precautions during dental procedures to prevent potential complications, such as adrenal crisis. The case highlights the importance of a multidisciplinary approach to ensure comprehensive care that addresses the specific needs of individuals with Allgrove Syndrome. Collaboration between dental professionals, endocrinologists, and other specialists is essential to provide appropriate treatment plans that optimize both oral and overall health outcomes for these patients.