A rare cause of dyspnea: Mounier Kuhn syndrome
Mounier-Kuhn syndrome, also known as tracheobronchomegaly, is a rare clinical and radiological condition characterized by tracheobronchial dilatation and recurrent respiratory infections. Patients may be asymptomatic or present with severe respiratory illnesses. A CT scan is sufficient to confirm the diagnosis. Treatment is symptomatic, and surgery is rarely indicated. We present the case of a 55-year-old patient with a 30-year history of chronic dyspnea, who presented with worsening shortness of breath, a productive cough, and episodes of bronchial superinfection. A chest CT scan, performed before and after contrast injection during both inspiratory and expiratory phases, confirmed the diagnosis of Mounier-Kuhn syndrome. This case aims to raise awareness of this rare condition and highlights a presentation where dyspnea is the primary symptom.
Authors
- Mouna Sabiri
- Mohamed Labied
- Ghizlane Lembarki (ORCID: https://orcid.org/0000-0001-6583-1866)
- Samira Lezar
- Feryal El Oualladi (ORCID: https://orcid.org/0000-0001-6555-1936)
- Chorouk Mountassir
- Ismail Bouzid
Institutions
- Centre Hospitalier Universitaire Ibn Rochd (MA)
- University of Hassan II Casablanca (MA)
Publication Details
- Journal
- Radiology Case Reports
- Published
- 2024-12-07
- DOI
- https://doi.org/10.1016/j.radcr.2024.11.015
- Primary Topic
- Tracheal and airway disorders
- Type
- article
- Field-Weighted Citation Impact
- 0.00